- Case Report
- A Case of Congenital Pulmonary Lymphangiectasia in Noonan Syndrome
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Dong Hee Lee, Won Bae Kim, Jung Hye Choi, Su Nam Lee
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Clin Exp Pediatr. 1997;40(6):877-882. Published online June 15, 1997
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Congenital pulmonary lymphangiectasia is a rare and perphaps underestimated cause of fatal
respiratory distress in the neonate or infant. Pathologically, this condition is characterized by wide
lymphatic channels in the subpleural and peribronchovascular spaces and the interlobular septa.
Noonan syndrome is characterized by a phenotype similar to Turner syndrome but with a normal
karyotype. Both pulmonary and intestinal lymphangiectasia have been reported in patients... |
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- A Case of Eosinophilic Fasciitis
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Dong Hee Lee, Jong Hyun Kim, Won Bae Lee, Jun Sung Lee
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Clin Exp Pediatr. 1996;39(1):120-125. Published online January 15, 1996
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Eosinophilic faciitis is a recently recognized entity causing inflammation, thickening and fibrosis of the fascia, which is associated with hypergammaglobulinemia, peripheral eosinolhila. This case of 11 year-old male patient who complaint migrating arthralgia and flexion contration with nodule on left upper extremity for 6 month and suddenly developed proptosis had hypergammaglobulinemia and elevated ESR. Biopsy of the nodule demonstrated inflammatory... |
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